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北京索萊寶科技有限公司
產(chǎn)品展廳
Anti-Desmin Polyclonal Antibody
  • 品牌:Solarbio
  • 產(chǎn)地:北京
  • 貨號:K106550P
  • 發(fā)布日期: 2019-05-13
  • 更新日期: 2025-07-11
產(chǎn)品詳請
產(chǎn)地 北京
品牌 Solarbio
保存條件 Store at -20°C. Avoid freeze / thaw cycles.
貨號 K106550P
應(yīng)用范圍 WB
CAS編號
抗體名 Anti-Desmin Polyclonal Antibody
克隆性 Polyclonal Antibody
靶點
適應(yīng)物種 Human Mouse Rat
形態(tài)
宿主 Rabbit
亞型 IgG
標(biāo)識物 CSM1;CSM2;LGMD2R;DES;Desmin
濃度 %
免疫原 A synthetic peptide of human Desmin
Defects in Desmin are the cause of desmin related cardio skeletal myopathy (CSM) also known as desmin related myopathy (DRM). CSM is characterized by skeletal muscle weakness associated with cardiac conduction blocks, arrhythmias, restrictive heart failure, and by intracytoplasmic accumulation of desmin reactive deposits in cardiac and skeletal muscle cells. A desmin related myopathy can have a distal onset, it is then known as hereditary distal myopathy (HDM). Defects in Desmin are also the cause of dilated cardiomyopathy type 1I (CMD1I). CMD1I is an autosomal form of dilated cardiomyopathy characterized by ventricular dilatation and impaired systolic function.
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