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北京索萊寶科技有限公司
產(chǎn)品展廳
Anti-SMPD1 Polyclonal Antibody
  • 品牌:Solarbio
  • 產(chǎn)地:北京
  • 貨號:K107041P
  • 發(fā)布日期: 2019-05-13
  • 更新日期: 2025-07-08
產(chǎn)品詳請
產(chǎn)地 北京
品牌 Solarbio
保存條件 Store at -20°C. Avoid freeze / thaw cycles.
貨號 K107041P
應(yīng)用范圍 IHC
CAS編號
抗體名 Anti-SMPD1 Polyclonal Antibody
克隆性 Polyclonal Antibody
靶點
適應(yīng)物種 Human Mouse Cow
形態(tài)
宿主 Rabbit
亞型 IgG
標識物 ASM;ASMASE;NPD;sphingomyelin phosphodiesterase
濃度 %
免疫原 A synthetic peptide of human SMPD1
The protein encoded by this gene is a lysosomal acid sphingomyelinase that converts sphingomyelin to ceramide. The encoded protein also has phospholipase C activity. Defects in this gene are a cause of Niemann-Pick disease type A (NPA) and Niemann-Pick disease type B (NPB). Multiple transcript variants encoding different isoforms have been identified.
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